RT Book, Section A1 Mehdi, Ali A1 Hajj-Ali, Rula A. A2 Dean, Steven M. A2 Satiani, Bhagwan A2 Abraham, William T. SR Print(0) ID 1105292645 T1 BEHÇET SYNDROME T2 Color Atlas and Synopsis of Vascular Diseases YR 2015 FD 2015 PB McGraw-Hill Medical PP New York, NY SN 9780071749541 LK accesscardiology.mhmedical.com/content.aspx?aid=1105292645 RD 2024/10/14 AB A 38-year-old Middle Eastern man presented to the emergency department complaining of sudden onset of chest pain associated with hemoptysis. Physical examination was notable for swelling in his right lower extremity. A provisional diagnosis of right leg DVT and secondary pulmonary embolism was suspected, and the patient underwent a computed tomography (CT) scan of the chest that revealed a 3-cm arterial aneurysm involving the right pulmonary artery (Figure 84-1). Further questioning revealed the patient had been suffering from recurrent painful oral aphthous ulcers for the past 5 years. He reported that the ulcers recurred around 6 times yearly. He also complained of two scrotal ulcers in the past 2 years. Moreover, the patient reported recurrent bilateral eye redness and pain over the past couple of years that were treated as conjunctivitis; no evaluation by an ophthalmologist was performed. This constellation of clinical symptoms, venous thrombosis, as well as the pulmonary aneurysms lead to the diagnosis of Behçet syndrome (BS)—a relapsing systemic vasculitis syndrome that can be as benign as isolated mucocutaneous lesions or be associated with significant morbidity and mortality as in this case.