RT Book, Section
A1 Litzendorf, Maria E.
A2 Dean, Steven M.
A2 Satiani, Bhagwan
A2 Abraham, William T.
SR Print(0)
ID 1105290754
T1 KLIPPEL-TRENAUNAY SYNDROME
T2 Color Atlas and Synopsis of Vascular Diseases
YR 2015
FD 2015
PB McGraw-Hill Medical
PP New York, NY
SN 9780071749541
LK accesscardiology.mhmedical.com/content.aspx?aid=1105290754
RD 2024/04/20
AB A  16-year-old  girl  presented  with  painful  right-leg  varicosities.  She  was  actively  involved  in  several  sports,  and  noticed  increasingly  painful  varicosities  in  her  posterior-lateral  thigh  and  extending  distally  down  to  her  foot.  Shortly  after  her  birth  purple-red  superficial  discoloration  along  her  right  leg  extending  up  to  her  flank  that  abruptly  terminated  prior  to  crossing  midline  was  identified.  Several  right  limb-shortening  procedures  were  required.  Initial  management  included  gradient  compression  hose  with  improvement  in  her  pain.  She  presented  several  years  later  with  worsening  symptoms  and  underwent  resection  of  her  symptomatic  vein  clusters  followed  by  targeted  sclerotherapy  several  months  postoperatively.  Figure  41-1  illustrates  a  typical  case  of  Klippel-Trenaunay  syndrome  (KTS).  While  generally  benign,  KTS  can  have  unusual  presentations  that  benefit  from  surgery,  sclerotherapy,  and/or  thermal  ablation  treatment.