RT Book, Section
A1 Grewal, Jasmine
A1 Opotowsky, Alexander R.
A2 Fuster, Valentin
A2 Narula, Jagat
A2 Vaishnava, Prashant
A2 Leon, Martin B.
A2 Callans, David J.
A2 Rumsfeld, John S.
A2 Poppas, Athena
SR Print(0)
ID 1202451290
T1 Anatomical and Physiological Classification of Adult Congenital Heart Disease
T2 Fuster and Hurst's The Heart, 15e
YR 2022
FD 2022
PB McGraw-Hill Education
PP New York, NY
SN 9781264257560
LK accesscardiology.mhmedical.com/content.aspx?aid=1202451290
RD 2024/04/19
AB Chapter  SummaryThis  chapter  describes  a  brief  history  of  classification  of  the  numerous  types  of  congenital  heart  disease  (CHD)  lesions  and  the  additive  value  of  approaches  (see  Fuster  and  Hurst's  Central  Illustration),  focusing  on  recent  developments  including  the  anatomic  and  physiologic  (AP)  classification  and  International  Pediatric  and  Congenital  Cardiac  Code  (IPCCC),  the  basis  for  ICD-11  codes.  Historically,  classification  has  focused  on  anatomy  based  on  pathology  investigations.  With  the  advent  of  surgical  options  for  CHD  management  in  the  20th  century,  attention  focused  on  distinctions  relevant  to  available  therapeutic  decisions.  These  surgeries,  and  later  catheter-based  treatments,  modify  the  initial  CHD,  often  transforming  the  pathophysiology  and  long-term  consequences.  As  more  individuals  survive  longer  with  CHD,  so  does  the  need  for  a  common  language  that  comprehensively  and  concisely  describes  not  only  the  underlying  congenital  heart  lesion,  but  also  prior  medical  interventions  repairs  and  cumulative  physiologic  burden.  Recent  classifications  have  explored  multiple  dimensions  to  characterizing  CHD.  The  recently  proposed  AP  classification  aims  to  represent  CHD  anatomy,  along  with  pertinent  interventions  and  current  physiologic  status.  This  provides  useful  nuance,  but  also  adds  complexity  and  associated  challenges.  Evolving  clinical  phenotype  requires  ongoing  modification,  but  these  classification  efforts  share  a  goal:  to  standardize  and  streamline  communication  and  thereby  improve  outcomes.