RT Book, Section
A1 Mehdi, Ali
A1 Hajj-Ali, Rula A.
A2 Dean, Steven M.
A2 Satiani, Bhagwan
A2 Abraham, William T.
SR Print(0)
ID 1105292645
T1 BEHÇET SYNDROME
T2 Color Atlas and Synopsis of Vascular Diseases
YR 2015
FD 2015
PB McGraw-Hill Medical
PP New York, NY
SN 9780071749541
LK accesscardiology.mhmedical.com/content.aspx?aid=1105292645
RD 2024/04/19
AB A  38-year-old  Middle  Eastern  man  presented  to  the  emergency  department  complaining  of  sudden  onset  of  chest  pain  associated  with  hemoptysis.  Physical  examination  was  notable  for  swelling  in  his  right  lower  extremity.  A  provisional  diagnosis  of  right  leg  DVT  and  secondary  pulmonary  embolism  was  suspected,  and  the  patient  underwent  a  computed  tomography  (CT)  scan  of  the  chest  that  revealed  a  3-cm  arterial  aneurysm  involving  the  right  pulmonary  artery  (Figure  84-1).  Further  questioning  revealed  the  patient  had  been  suffering  from  recurrent  painful  oral  aphthous  ulcers  for  the  past  5  years.  He  reported  that  the  ulcers  recurred  around  6  times  yearly.  He  also  complained  of  two  scrotal  ulcers  in  the  past  2  years.  Moreover,  the  patient  reported  recurrent  bilateral  eye  redness  and  pain  over  the  past  couple  of  years  that  were  treated  as  conjunctivitis;  no  evaluation  by  an  ophthalmologist  was  performed.  This  constellation  of  clinical  symptoms,  venous  thrombosis,  as  well  as  the  pulmonary  aneurysms  lead  to  the  diagnosis  of  Behçet  syndrome  (BS)—a  relapsing  systemic  vasculitis  syndrome  that  can  be  as  benign  as  isolated  mucocutaneous  lesions  or  be  associated  with  significant  morbidity  and  mortality  as  in  this  case.